Educating Students with Prader-Willi Syndrome


  • Colin Reilly


PWS, Prader-Willi Syndrome, Neurodevelopmental Disorder, Genetic Condition


Prader-Willi Syndrome (PWS) is a complex genetic condition characterised by a propensity to abnormal and excessive eating behaviour and a range of medical and behavioural features. There is also evidence of a distinctive cognitive profile which has implications for how the affected children learn. Having an understanding of the cognitive and behavioural profile of PWS is essential in helping affected children reach their potential in educational settings.


Bertella, L., Girelli, L., Grugni, G., Marchi, S., Molinari, E. and Semenza, C. (2005) Mathematical Skills in Prader-Willi Syndrome, Journal of Intellectual Disability Research, Vol. 49 (2), pp. 159-169.

Butler, M.G. and Meaney, F.J. (1991) Standards for Selected Anthropometric Measures in Prader-Willi Syndrome, Pediatrics, Vol. 88, pp. 853-860.

Cassidy, S.B. and McCandless, S.E. (2005) Prader-Willi Syndrome. In Cassidy, S.B. and Allanson, J.E. (eds) Management of Genetic Syndromes (2nd ed), New Jersey: John Wiley and Sons, pp. 429-448.

Chedd, N., Levine, K. and Wharton, R.H. (2006) Educational Considerations for Children with Prader-Willi Syndrome. In Butler, M.G., Lee, P.D.K. and Whitman, B.Y. (eds) Management of Prader-Willi Syndrome (3rd ed), New York: Springer, pp. 302-316.

REACH Journal of Special Needs Education in Ireland, Vol. 23.1 (2009), 13–238

Curfs, L.M.G. (1992) Psychological Profile and Behavioral Characteristics in PraderWilli Syndrome. In S.B. Cassidy (ed.) Prader-Willi Syndrome and Other 15q Deletion Disorders, Berlin: Springer-Verlag, pp. 211-222.

Dimitropoulous, A., Feurer, I.D., Butler, M.G. and Thompson, T. (2001) Emergence of Compulsive Behaviour and Tantrums in Children with Prader-Willi Syndrome, American Journal on Mental Retardation, Vol. 106, pp. 39-51.

Dykens, E.M., Hodapp, R.M., Walsh, K. and Nash, L.J. (1992) Profiles, Correlates, and Trajectories of Intelligence in Prader-Willi Syndrome, Journal of the Academy of Child and Adolescent Psychiatry, Vol. 31, pp. 1125-1130.

Dykens, E.M., Leckman, J. and Cassidy, S.B. (1996) Obsessions and Compulsions in Prader-Willi Syndrome, Journal of Child Psychology and Psychiatry, Vol. 37, pp. 995-1002.

Dykens, E.M., Hodapp, R.M. and Finucane, B. (2000) Genetics and Mental Retardation Syndromes: A New Look at Behaviour and Interventions, Baltimore: Brookes.

Eihozler, U., Gellatly, M., Lee, P.K., Ritzen, M. and Whitman, B.Y. (2001) A Comprehensive Team Approach to the Management of Prader Willi Syndrome, Costozza, Italy: International Prader-Willi Syndrome Organization (IPWSO).

Gillessen-Kaesbach, G., Robinson, W., Lohmann, D., Kaya-Westerloh, S., Passarge, E. and Horstthemke, B. (1995) Genotype-phenotype Correlation in a Series of 167 Deletion and Non-deletion Patients with Prader-Willi Syndrome, Human Genetics, Vol. 96, pp. 638-643.

Greenswag, L.R. (1987) Adults with Prader-Willi Syndrome: A Survey of 232 Cases, Developmental Medicine and Child Neurology, Vol. 29, pp. 145-152.

Holland, A.J., Treasure, J., Coskeran, P., Dallow, J., Milton, N. and Hillhouse, E. (1993) Measurement of Excessive Appetite and Metabolic Changes in Prader-Willi Syndrome, International Journal of Obesity, Vol. 17, pp. 526-532.

Holm, V.A., Cassidy, S.B., Butler, M.G., Hanchett, J.M., Greenswag, L.R., Whitman, B.Y. and Greenberg, F. (1993) Prader-Willi Syndrome: Consensus Diagnostic Criteria, Pediatrics, Vol. 91, pp. 398-402.

Lewis, B.A. (2006) Speech and Language Disorders Associated with Prader-Willi Syndrome. In Butler, M.G., Lee, P.D.K. and Whitman, B.Y. (eds) Management of Prader-Willi Syndrome (3rd ed), New York: Springer, pp. 272-283.

Milner, K.M., Craig, E.E., Thompson, R.J., Veltmann, M.W.M., Thomas, N.S., Roberts, S., Bellamy, M., Curran, S.R., Sporikou, M.J. and Bolton, P.F. (2005)

Prader-Willi Syndrome: Intellectual Abilities and Behavioural Features by Genetic Subtype, Journal of Child Psychology and Psychiatry, Vol. 46 (10), pp. 1089-1096.

Prader-Willi Syndrome Association, United Kingdom (PWSA, UK) (2006) Educating the Child with Prader-Willi Syndrome – A Guide for Teachers, Educational Care Assistants and Others Concerned with the Education of a Child with PWS, London: PWSA, UK.

Reddy, L.A. and Pfeiffer, S.I. (2007) Behavioral and Emotional Symptoms of Children and Adolescents with Prader-Willi Syndrome, Journal of Autism and Developmental Disorders, Vol. 37, pp. 830-839.

Swaab, D.F., Purba, J.S. and Hofman, M.A. (1995) Alterations in the Hypothalamus Paraventricular Nucleus and its Oxytocin Neurons (Putative Satiety Cells) in Prader-Willi Syndrome - A Study of Five Cases, Journal of Clinical Endocrinology and Metabolism, Vol. 80, pp. 573-579.

Whitman, B.Y. and Jackson, K. (2006) Tools for Psychological and Behavioral Management. In Butler, M.G., Lee, P.D.K. and Whitman, B.Y. (eds) Management of Prader-Willi Syndrome (3rd ed), New York: Springer, pp. 317-343.

Whittington, J. and Holland, T. (2004) Prader-Willi Syndrome: Development and Manifestation. Cambridge: Cambridge University Press.




How to Cite

Reilly, C. (2009). Educating Students with Prader-Willi Syndrome. REACH: Journal of Inclusive Education in Ireland, 23(1), 13–23. Retrieved from